Abstract

Head computed tomography (CT) scan showed bilateral caudate atrophy [Figure 1]a. Magnetic resonance imaging (MRI) brain showed bilaterally symmetrical hypo-intensities in globus pallidus, substantia nigra, and red nucleus on T2- and susceptibility-weighted images along with caudate and posterior putaminal atrophy [Figure 1]b-d. MRI of the brain in PKAN shows the classic 'eye-of-the-tiger' appearance, attributed to iron deposition in the globus pallidus, which causes a proton relaxation effect, resulting in a decrease in T1 and T2 relaxation times and decreased signal intensity in the globus pallidus, while the central hyper-intensity is attributed to intense gliosis.

Details

Title
Mineral deposition on magnetic resonance imaging in chorea-acanthocytosis: A pathogenic link with pantothenate kinase-associated neurodegeneration?
Author
Kaul, Bhavna; Goyal, Vinay; Shukla, Garima; Srivastava, Achal; Garg, Ajay; Bader, Benedikt; Danek, Adrian; Hayflick, Susan; Behari, Madhuri
Pages
169-70
Publication year
2013
Publication date
Mar-Apr 2013
Publisher
Medknow Publications & Media Pvt. Ltd.
ISSN
00283886
e-ISSN
19984022
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
1353556122
Copyright
Copyright Medknow Publications & Media Pvt Ltd Mar-Apr 2013