Content area

Abstract

Schnitzler syndrome is a rare acquired systemic disease with a chronic evolution and difficult treatment. We report a 50-year-old woman with Schnitzler syndrome for 10 years, with major impact on her quality of life and refractory to conventional therapies. The patient was started on anakinra, an IL-1 receptor antagonist, with a rapid and sustained remission of the syndrome manifestations.

Details

Title
Schnitzler Syndrome: A Dramatic Response to Anakinra
Author
Gouveia, Ana Isabel 1 ; Micaelo, Manuela 2 ; Pierdomenico, Francesca 3 ; Freitas, João Pedro 1 

1  University Clinic of Dermatology, Hospital de Santa Maria, Lisbon, Portugal (GRID:grid.411265.5) (ISNI:0000 0001 2295 9747) 
2  Instituto Português de Reumatologia, Lisbon, Portugal (GRID:grid.411265.5) 
3  Instituto Português de Oncologia de Lisboa, Francisco Gentil, Department of Hematology, Lisbon, Portugal (GRID:grid.418711.a) (ISNI:0000000406310608) 
Pages
299-302
Publication year
2016
Publication date
Jun 2016
Publisher
Springer Nature B.V.
ISSN
21938210
e-ISSN
21909172
Source type
Scholarly Journal
Language of publication
English
DOI
https://doi.org/10.1007/s13555-016-0108-7
ProQuest document ID
1796136366
Copyright
Copyright Springer Nature B.V. Jun 2016