Abstract

We report a case of hypoplastic left heart syndrome with an anomalous left coronary artery from the pulmonary artery (ALCAPA) identified intraoperatively during the Stage-II palliation. Due to recurring ventricular fibrillation on sternotomy, a hybrid Stage-I palliation was performed. During comprehensive Stage-II, the ALCAPA was reimplanted in the neoaorta and measures, including a nontraditional Damus connection/arch reconstruction and classic bilateral Glenn procedures, were taken to avoid compression of the coronary artery. After a successful Fontan procedure, he continues to do well at 5 years old, becoming the first patient reported in the literature to survive all the three stages of single-ventricle palliation.

Details

Title
First report of successfully palliating a hypoplastic left heart syndrome patient with anomalous left coronary artery from the pulmonary artery beyond fontan
Author
Riggs, Kyle 1 ; Price, Nina 1 ; Szugye, Nicholas 1 ; Goldstein, Bryan 1 ; Morales, David S 1 

 Cincinnati Children's Hospital Medical Center, Heart Institute, Cincinnati, OH 
Pages
318-320
Publication year
2019
Publication date
Sep-Dec 2019
Publisher
Medknow Publications & Media Pvt. Ltd.
ISSN
09742069
e-ISSN
09745149
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
2276722015
Copyright
© 2019. This work is published under https://creativecommons.org/licenses/by-nc-sa/4.0/ (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.