Abstract

[...]while the typical presentation of EFT is that of classic ES (i.e., primary tumour of a long bone presenting in childhood; monotonous cytomorphology with diffuse and strong CD99 expression; sensitivity to intensified chemotherapy and radiotherapy), there is significant variability in the histopathological characteristics and clinical behaviour of EFT that remains incompletely described by any association with specific EWSR1 rearrangements[5]. [...]the subset of SRCSs that bear histopathological similarity to EFT but do not harbour EWSR1 fusions have been classified as Ewing-like sarcomas, a heterogeneous group of cancers that frequently exhibit clinical characteristics atypical for classic ES and are associated with primary chemoresistance and poor survival outcomes[2]. [...]there were limits to the sensitivity of PCR-based approaches in detecting fusion transcripts.

Details

Title
Ewing-like sarcomas: New molecular diagnoses in need of optimized treatment approaches
Author
Lee, Alex 1 ; Huang, Paul 2 ; Jones, Robin 3 

 Sarcoma Department, Royal Marsden; Division of Molecular Pathology, Institute of Cancer Research, London 
 Division of Molecular Pathology, Institute of Cancer Research, London 
 Sarcoma Department, Royal Marsden; Division of Clinical Studies, Institute of Cancer Research, London 
Pages
521-523
Publication year
2019
Publication date
Dec 2019
Publisher
Scientific Scholar
ISSN
0971-5916
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
2351350208
Copyright
© 2019. This work is published under https://creativecommons.org/licenses/by-nc-sa/4.0/ (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.