Abstract

Blastic plasmacytoid dendritic cell neoplasm is a rare, aggressive tumor characterized by skin and/or marrow infiltration by CD4+ CD56+ cells. Historically, the tumor was variably thought to arise from either monocytes, T cells or NK cells giving rise to terms such as CD4+/CD56+ acute monoblastic leukemia, primary cutaneous CD4+/CD56+ hematodermic tumor and blastic NK-cell lymphoma. Whilst considerable progress has been made in understanding the histogenesis, the best modality of treatment remains to be defined. We are therefore reporting this case which was successfully treated with a T-deplete allogeneic transplant and the patient is currently alive and in remission 4 years post transplant.

Details

Title
Reduced intensity allogeneic stem cell transplant for treatment of blastic plasmacytoid dendritic cell neoplasm
Author
Lokare, Anand; Nikolousis, Emmanouil; Phillips, Neil; Rudzki, Zbignieuw; Lovell, Richard; Kishore, Bhuvan; Milligan, Don; Paneesha, Shankara
Section
Case Reports
Publication year
2014
Publication date
Jan 2014
Publisher
MDPI AG
ISSN
20388322
e-ISSN
20388330
Source type
Scholarly Journal
Language of publication
Italian; English
ProQuest document ID
2438810407
Copyright
© 2014. This work is published under http://creativecommons.org/licenses/by-nc/4.0/ (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.