Abstract

Due to the variability in clinical phenotypes, it is difficult to classify sub-types simply by clinical features; therefore, molecular and genetic analyses are the most reliable methods for confirming diagnosis, carrier screening, and pre-natal diagnosis. [4] A total of 12 unrelated patients with OCA were selected for this study who had only one allelic point mutation detectable by Sanger sequencing or NGS in either the tyrosinase (TYR) or oculocutaneous albinism II (OCA2) gene. All mutations were graded as pathogenic variations according to the standards and guidelines for the interpretation of sequence variants published by the American College of Medical Genetics and Genomics,[5] and two of these were de novo mutations [Table 1].Table 1 Genotypes of the 12 patients with oculocutaneous albinism.

Details

Title
Application of multiplex ligation-dependent probe amplification in the genetic testing of oculocutaneous albinism
Author
Ying-Zi, Zhang 1 ; Da-Yong, Bai 2 ; Zhan, Qi 3 ; Su-Zhou, Zhao 4 ; Xiu-Min, Yang 5 ; Li, Wei 6 ; Ai-Hua, Wei 5 

 Department of Dermatology, Beijing Tongren Hospital, Capital Medical University, Beijing 100730, China; Shunyi Women and Children's Hospital of Beijing Children's Hospital, Beijing 101300, China 
 Department of Ophthalmology, Beijing Children's Hospital, Capital Medical University, National Center for Children's Health, Beijing 100045, China 
 Laboratory for Genetics of Birth Defects, Beijing Pediatric Research Institute, Beijing Children's Hospital, Capital Medical University, National Center for Children's Health, Beijing 100045, China 
 Fulgent Technologies Incorporated, Shanghai 201404, China 
 Department of Dermatology, Beijing Tongren Hospital, Capital Medical University, Beijing 100730, China 
 Shunyi Women and Children's Hospital of Beijing Children's Hospital, Beijing 101300, China; Laboratory for Genetics of Birth Defects, Beijing Pediatric Research Institute, Beijing Children's Hospital, Capital Medical University, National Center for Children's Health, Beijing 100045, China 
Pages
2011-2012
Section
Correspondence
Publication year
2019
Publication date
Aug 2019
Publisher
Lippincott Williams & Wilkins Ovid Technologies
ISSN
03666999
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
2502607748
Copyright
Copyright © 2019 The Chinese Medical Association, produced by Wolters Kluwer, Inc. under the CC-BY-NC-ND license. This work is published under http://creativecommons.org/licenses/by-nc-nd/4.0 (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.