Abstract

We studied the scientific literature and disease guidelines in order to summarize the clinical utility of genetic testing for familial exudative vitreoretinopathy (FEVR). There is insufficient data to determine the prevalence of FEVR. Variations in the FZD4 (OMIM gene: 604579; OMIM disease: 133780), TSPAN12 (OMIM gene: 613138; OMIM disease: 613310) and ZNF408 (OMIM gene: 616454; OMIM disease: 616468) genes have autosomal dominant inheritance, whereas variations in LRP5 (OMIM gene: 603506; OMIM disease: 601813) have autosomal dominant or recessive inheritance and variations in NDP (OMIM gene: 300658; OMIM disease: 305390) have X-linked inheritance. Clinical diagnosis is based on clinical findings, family history, ophthalmological examination, fundoscopy, slit-lamp examination and fluorescein angiography. The genetic test is useful for confirming diagnosis and for differential diagnosis, couple risk assessment and access to clinical trials.

Details

Title
Genetic testing for familial exudative vitreoretinopathy
Author
Abeshi, Andi 1 ; Marinelli, Carla 2 ; Beccari, Tommaso 3 ; Dundar, Munis 4 ; Colombo, Leonardo 5 ; Bertelli, Matteo 6 

 MAGI Balkans, Tirana, Albania; MAGI’S Lab, Rovereto, Italy 
 MAGI’S Lab, Rovereto, Italy 
 Department of Pharmaceutical Sciences, University of Perugia, Perugia, Italy 
 Department of Medical Genetics, Erciyes University Medical School, Kayseri, Turkey 
 Department of Ophthalmology, ASST Santi Paolo e Carlo, University of Milan, Milan, Italy 
 MAGI’S Lab, Rovereto, Italy; MAGI Euregio, Bolzano, Italy 
Pages
51-53
Publication year
2017
Publication date
2017
Publisher
De Gruyter Poland
e-ISSN
2564615X
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
3156966123
Copyright
© 2017. This work is published under http://creativecommons.org/licenses/by-nc-nd/4.0 (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.