Abstract

We report the case of a 37-year-old woman who presented with progressive renal dysfunction and proteinuria, in whom renal biopsy confirmed a diagnosis of AA amyloidosis. No evidence of chronic suppurative infection, connective tissue disease or malignancy was found. A past history of Langerhans cell histiocytosis (LCH) diagnosed in childhood was noted for which the patient had been successfully treated with surgical excision, corticosteroids, radiotherapy and chemotherapy. Renal disease in LCH is not widely recognized and thus we describe a patient with LCH in whom AA amyloidosis developed in the absence of any other established cause.

Details

Title
AA amyloidosis in a patient with Langerhans cell histiocytosis
Author
Thomson, Peter C 1 ; Taylor, Alison HM 1 ; Morris, Scott TW 1 ; Kipgen, David 2 ; Mactier, Robert A 1 

 Renal Unit, Glasgow Royal Infirmary, Glasgow, UK 
 Department of Pathology, Western Infirmary, Glasgow, UK 
Pages
104-106
Publication year
2011
Publication date
Apr 2011
Publisher
Oxford University Press
ISSN
17530784
e-ISSN
17530792
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
3170099592
Copyright
© The Author 2011. Published by Oxford University Press on behalf of ERA-EDTA. All rights reserved. For permissions, please e-mail: [email protected]. This work is published under http://creativecommons.org/licenses/by-nc/4.0/ (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.