Abstract

The HMG-CoA reductase degradation protein 1 (HRD1) has been identified as a key enzyme for endoplasmic reticulum-associated degradation of misfolded proteins, but its organ-specific physiological functions remain largely undefined. Here we show that mice with HRD1 deletion specifically in the liver display increased energy expenditure and are resistant to HFD-induced obesity and liver steatosis and insulin resistance. Proteomic analysis identifies a HRD1 interactome, a large portion of which includes metabolic regulators. Loss of HRD1 results in elevated ENTPD5, CPT2, RMND1, and HSD17B4 protein levels and a consequent hyperactivation of both AMPK and AKT pathways. Genome-wide mRNA sequencing revealed that HRD1-deficiency reprograms liver metabolic gene expression profiles, including suppressing genes involved in glycogenesis and lipogenesis and upregulating genes involved in glycolysis and fatty acid oxidation. We propose HRD1 as a liver metabolic regulator and a potential drug target for obesity, fatty liver disease, and insulin resistance associated with the metabolic syndrome.

Details

Title
ER-associated ubiquitin ligase HRD1 programs liver metabolism by targeting multiple metabolic enzymes
Author
Wei, Juncheng 1 ; Yuan, Yanzhi 2 ; Chen, Lu 3 ; Xu, Yuanming 1 ; Zhang, Yuehui 2 ; Wang, Yajun 1 ; Yang, Yanjie 4 ; Clara Bien Peek 5 ; Diebold, Lauren 6 ; Yang, Yi 1 ; Gao, Beixue 1 ; Jin, Chaozhi 2 ; Melo-Cardenas, Johanna 1 ; Chandel, Navdeep S 6 ; Zhang, Donna D 7 ; Pan, Hui 3 ; Zhang, Kezhong 8 ; Wang, Jian 2 ; He, Fuchu 2 ; Fang, Deyu 1 

 Department of Pathology, Northwestern University Feinberg School of Medicine, Chicago, IL, USA 
 State Key Laboratory of Proteomics, Beijing Proteome Research Center, National Center for Protein Sciences (Beijing), Beijing Institute of Lifeomics, Beijing, China 
 Department of Endocrinology, Peking Union Medical College Hospital, Chinese Academy of Medical Science, Beijing, China 
 Department of Medical Psychology, Public Health Institute of Harbin Medical University, Harbin, China 
 Division of Endocrinology, Metabolism and Molecular Medicine, Department of Medicine, Northwestern University Feinberg School of Medicine, Chicago, IL, USA 
 Department of Medicine, Northwestern University Feinberg School of Mdicine, Chicago, IL, USA 
 Department of Pharmacology and Toxicology, University of Arizona, Tucson, AZ, USA 
 Center for Molecular Medicine and Genetics, Department of Biochemistry, Microbiology, and Immunology, Wayne State University School of Medicine, Detroit, MI, USA 
Pages
1-14
Publication year
2018
Publication date
Sep 2018
Publisher
Nature Publishing Group
e-ISSN
20411723
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
2101994084
Copyright
© 2018. This work is published under http://creativecommons.org/licenses/by/4.0/ (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.