Abstract

Acanthosis nigricans (AN) describes clinically hyperpigmented skin, which most commonly affects the flexural areas such as axilla, groin and neck. It is usually a benign condition associated with obesity, insulin resistance, and hyperinsulinemia; endocrinopathy; or malignancy, in particular, gastrointestinal adenocarcinoma. It can also occur in association with various genetic syndromes involving various organ systems. Few such known syndromes are Berardinelli-Seip syndrome, Alström syndrome, Leprechaunism, and Bardet-Biedl syndrome. MORFAN syndrome, which associates mild mental retardation, pre- and post-natal overgrowth, remarkable facies and diffuse and widespread AN, is a rare entity.

Details

Title
MORFAN syndrome: A rarity but a reality!
Author
Roy, Gourab 1 ; Sen, Sumit 1 ; Poddar, Shreya 1 

 Department of Dermatology, Institute of Post Graduate Medical Education and Research and SSKM Hospital, Bhowanipore, Kolkata, West Bengal 
Pages
231-234
Publication year
2019
Publication date
May/Jun 2019
Publisher
Medknow Publications & Media Pvt. Ltd.
ISSN
00195154
e-ISSN
19983611
Source type
Scholarly Journal
Language of publication
English
ProQuest document ID
2231789456
Copyright
© 2019. This work is published under https://creativecommons.org/licenses/by-nc-sa/4.0/ (the “License”). Notwithstanding the ProQuest Terms and Conditions, you may use this content in accordance with the terms of the License.