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The acceptability and feasibility of a homebased gestural training program for nine children with Angelman syndrome (AS), deletion positive, and their parents were examined. Children with AS have been found to exhibit a variety of challenges, including severe communication disabilities for which different Augmentative and Alternative Communication (AAC) systems have been of limited use (Alvares & Downing, 1998). Parents in this study were taught to recognize and then enhance their children's use of natural gestures as enhanced natural gestures (ENGs). ENGs are intentional behaviors that are present in a child's motor repertoire or can be easily taught based on a child's extant motor skills. Unlike contact gestures, such as grabbing objects from partners or pulling partners toward preferred activities, ENGs do not require physical contact with entities or interactants
and are readily understood by others in context.
Parents were taught to use four primary teaching techniques: environmental sabotage, mand-model, expectant delay, and molding/ shaping, and then to use these techniques over a period of 16 to 18 weeks to foster their child's use of ENGs. A questionnaire Enhanced Natural Gestures-Acceptability Rating Form (ENG-ARF), was administered to sample parents' perceptions about the acceptability and feasibility of the ENG training program. With few exceptions, parents described this method as acceptable, effective, reasonable, and easy to teach others, with minor negative consequences and side effects. Implications for subsequent research are discussed.
Key Words: gestures, Angelman syndrome, augmentative and alternative communication, parent instruction, home-based program
This study examined the acceptability and feasibility of a home-based intervention program involving enhanced natural gestures (defined later) as implemented by the parents of nine children with Angelman syndrome. It was approximately 35 years ago that Dr. Harry Angelman, an English physician, described three children who shared a number of characteristics (Angelman, 1965). These included severe mental retardation, seizures, ataxia, an absence of speech, easily provoked laughter, and dysmorphic facial features. The syndrome, initially referred to as `Happy Puppet Syndrome' was subsequently labeled Angelman syndrome (AS), in honor of its discoverer (Williams & Frias, 1982).
Although AS was first thought to be rare, advances in genetic testing have resulted in investigators revising estimates of its incidence from 1 in 20,000 live births (Chan et al, 1993; Clayton-Smith & Pembrey, 1992) to,...